Polysplenia/Heterotaxy Syndrome Associated With Aortic Coarctation and Multiple Venous Anomalies: Multidetector Computed Tomography Findings

Karadeniz A., Oysu A., Sahin S.

VASCULAR AND ENDOVASCULAR SURGERY, vol.44, no.5, pp.381-384, 2010 (SCI-Expanded) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 44 Issue: 5
  • Publication Date: 2010
  • Doi Number: 10.1177/1538574410370789
  • Journal Name: VASCULAR AND ENDOVASCULAR SURGERY
  • Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Page Numbers: pp.381-384
  • Keywords: polysplenia syndrome, heterotaxy syndrome, aortic coarctation, venous abnormality
  • Marmara University Affiliated: No

Abstract

Polysplenia/heterotaxy syndrome is a rare condition involving multiple gastrointestinal, vascular, and cardiac malformations. We present a previously unreported association of aortic coarctation, double superior vena cava, a left-hand side inferior vena cava with hemiazygos vein continuation and a right retroaortic renal vein with polysplenia/heterotaxy syndrome. Multidetector computed tomography with multiplanar reconstruction images were useful in the detection of these abnormalities.