Management of primary ciliary dyskinesia in European children: recommendations and clinical practice


Strippoli M. F., Frischer T., Barbato A., Snijders D., Maurer E., Lucas J. S. A., ...Daha Fazla

EUROPEAN RESPIRATORY JOURNAL, cilt.39, sa.6, ss.1482-1491, 2012 (SCI-Expanded) identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 39 Sayı: 6
  • Basım Tarihi: 2012
  • Doi Numarası: 10.1183/09031936.00073911
  • Dergi Adı: EUROPEAN RESPIRATORY JOURNAL
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Sayfa Sayıları: ss.1482-1491
  • Anahtar Kelimeler: Bronchiectasis, ciliary motility disorders, diagnosis, Kartagener syndrome, primary ciliary dyskinesia, therapy, DIAGNOSIS, STATE
  • Marmara Üniversitesi Adresli: Evet

Özet

The European Respiratory Society Task Force on primary ciliary dyskinesia (PCD) in children recently published recommendations for diagnosis and management. This paper compares these recommendations with current clinical practice in Europe.