Management of primary ciliary dyskinesia in European children: recommendations and clinical practice


Strippoli M. F., Frischer T., Barbato A., Snijders D., Maurer E., Lucas J. S. A., ...More

EUROPEAN RESPIRATORY JOURNAL, vol.39, no.6, pp.1482-1491, 2012 (SCI-Expanded) identifier

  • Publication Type: Article / Article
  • Volume: 39 Issue: 6
  • Publication Date: 2012
  • Doi Number: 10.1183/09031936.00073911
  • Journal Name: EUROPEAN RESPIRATORY JOURNAL
  • Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Page Numbers: pp.1482-1491
  • Keywords: Bronchiectasis, ciliary motility disorders, diagnosis, Kartagener syndrome, primary ciliary dyskinesia, therapy, DIAGNOSIS, STATE
  • Marmara University Affiliated: Yes

Abstract

The European Respiratory Society Task Force on primary ciliary dyskinesia (PCD) in children recently published recommendations for diagnosis and management. This paper compares these recommendations with current clinical practice in Europe.