Detection of a rare cause of pulmonary hypertension by multimodality imaging: Left ventricular endomyocardial fibrosis

Uygur B., Turkvatan Cansever A., Demir A. R., Kahraman S., Guner A., ŞAHİN A. A., ...More

Journal of Clinical Ultrasound, vol.49, no.5, pp.520-524, 2021 (SCI-Expanded) identifier identifier

  • Publication Type: Article / Article
  • Volume: 49 Issue: 5
  • Publication Date: 2021
  • Doi Number: 10.1002/jcu.23003
  • Journal Name: Journal of Clinical Ultrasound
  • Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus, Biotechnology Research Abstracts, CINAHL, EMBASE, MEDLINE
  • Page Numbers: pp.520-524
  • Keywords: cardiac magnetic resonance, echocardiography, endomyocardial fibrosis, multimodality imaging, pulmonary hypertension
  • Marmara University Affiliated: Yes

Abstract

Endomyocardial fibrosis (EMF), a restrictive cardiomyopathy characterized by subendocardial fibrosis, is commonly seen in tropical and subtropical regions. EMF involving the left ventricle presents with severe pulmonary hypertension (PH) and is a rare cause of PH in non-tropical areas. Multimodality imaging is important for accurate diagnosis, especially cardiac magnetic resonance imaging which is the cornerstone. Herein, we report the case of a patient who presented with heart failure symptoms and severe PH, and in whom EMF was diagnosed by multimodality imaging.