Polyarteritis nodosa in case of familial Mediterranean fever


GÖKCE İ. , Altuntaş Ü., FİLİNTE D. , ALPAY H.

TURKISH JOURNAL OF PEDIATRICS, cilt.60, sa.3, ss.326-330, 2018 (SCI İndekslerine Giren Dergi) identifier identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 60 Konu: 3
  • Basım Tarihi: 2018
  • Doi Numarası: 10.24953/turkjped.2018.03.016
  • Dergi Adı: TURKISH JOURNAL OF PEDIATRICS
  • Sayfa Sayıları: ss.326-330

Özet

Familial Mediterranean fever (FMF) is an autosomal recessive disease characterized by recurrent self-limited attacks of fever accompanied by peritonitis, pleuritis, and arthritis. Protracted febrile myalgia syndrome (PFMS) is a rare form of vasculitic disease which is an uncommon dramatic manifestation of FMF, characterized by severe crippling myalgia and high fever. Polyarteritis nodosa (PAN) is a systemic necrotizing vasculitis affecting medium or small arteries. It is rarely observed in children, but its incidence increases in the presence of FMF. In this article we described a 14-yea-old child diagnosed with FMF associated with PAN. Physicians should be aware of this possible association.