HEREDITARY HEMORHAGIC TELANGIECTASIA: A RARE CAUSE OF HEPATIC ENCEPHALOPATHY DUE TO PORTOSYSTEMIC SHUNT


Akpinar T. S. , Kose M., Iliaz R., Evirgan S., Bulakci M., Yilmaz E., ...More

NOBEL MEDICUS, vol.11, no.3, pp.74-76, 2015 (Journal Indexed in ESCI) identifier identifier

  • Publication Type: Article / Article
  • Volume: 11 Issue: 3
  • Publication Date: 2015
  • Title of Journal : NOBEL MEDICUS
  • Page Numbers: pp.74-76

Abstract

Hepatic encephalopathy is a common complication of end-stage liver disease. It happens in the presence of significant hepatic dysfunction and the diversion of the portal blood to the systemic circulation (porto-systemic shunts). Hereditary Hemorrhagic Telangiectasia (HHT) or Osler-Weber-Rendu disease, can also involve the liver along with the skin, mucous membranes, lung, brain, and gastrointestinal tract. The prevalence of hepatic involvement in HHT ranges between 41% and 78%. Although most patients with HHT are asymptomatic, some may have symptoms due to high-output heart failure, portal hypertension and biliary disease. Less commonly, patients may also develop porto-systemic encephalopathy. In this case report, we present a woman aged 63 years, who was diagnosed as having hepatic encephalopathy due to a portosystemic shunt.