A Case of Peutz-Jeghers Syndrome Presenting With an Inoperable Periampullary Tumor

Ergenc M., UPRAK T. K.

CUREUS, cilt.13, sa.4, 2021 (ESCI) identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 13 Sayı: 4
  • Basım Tarihi: 2021
  • Doi Numarası: 10.7759/cureus.14359
  • Dergi Adı: CUREUS
  • Derginin Tarandığı İndeksler: Emerging Sources Citation Index (ESCI)
  • Anahtar Kelimeler: peutz-jeghers syndrome, periampullary tumors, gastric outlet obstruction
  • Marmara Üniversitesi Adresli: Evet

Özet

Peutz-Jeghers syndrome (PJS) is a syndrome characterized by multiple hamartomatous polyps in the gastrointestinal system and melanin pigments accumulating in the skin and mucous membranes. Patients with PJS have an increased risk of gastrointestinal malignancies. In this syndrome, pancreatic cancer is primarily detected in older ages. In this article, we present a case of a patient with an unresectable periampullary tumor and PJS.