Inspiratory Muscle Training in Late-Onset Pompe Disease: The Effects on Pulmonary Function Tests, Quality of Life, and Sleep Quality

Aslan G. K., ERSÖZ HÜSEYİNSİNOĞLU B., Oflazer P., GÜRSES H. N., KIYAN E.

LUNG, cilt.194, sa.4, ss.555-561, 2016 (SCI-Expanded) identifier identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 194 Sayı: 4
  • Basım Tarihi: 2016
  • Doi Numarası: 10.1007/s00408-016-9881-4
  • Dergi Adı: LUNG
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Sayfa Sayıları: ss.555-561
  • Anahtar Kelimeler: Pompe diseases, Pulmonary functions, Inspiratory muscle training, Diaphragm weakness, Sleep quality, Quality of life, RESPIRATORY-FAILURE, NATURAL COURSE, CHILDREN, GLYCOGENOSIS, MANAGEMENT, DIAGNOSIS, THERAPY, VALUES, FALL, RMT
  • Marmara Üniversitesi Adresli: Hayır

Özet

Late-onset Pompe disease (LOPD) is characterized by progressive skeletal and respiratory muscle weakness. Little is known about the effect of inspiratory muscle training (IMT) on pulmonary function in subjects with LOPD. The aim of the present study was to investigate the effect of an 8-week IMT program on pulmonary function tests, quality of life, and sleep quality in eight patients with LOPD who were receiving enzyme replacement therapy (ERT).